Logo

American Heart Association

  18
  0


Final ID: MP1386

Right Axillary Thoracotomy for Repair of a Complex Coronary Triad in the Youngest Known Infant: Right Coronary and Sinus Node Artery Aneurysms With Dual Fistulas to the Right Atrium

Abstract Body (Do not enter title and authors here): Case
A 4-month-old female infant presented with cough and fever. A cardiac murmur was noted at the pulmonary valve area. Lab tests revealed mildly elevated WBC and CRP. CXR was unremarkable. TTE showed a markedly dilated RCA ostium (6.8 mm) and a saccular aneurysm arising from the proximal RCA communicating with the RA. Contrast-enhanced CCTA with 3D reconstruction confirmed an RCA ostial diameter of 5.5 mm, a 7 mm SNA aneurysm draining into the RA through two fistulas (2.0 mm and 2.5 mm). There were no clinical or laboratory findings suggestive of Kawasaki disease (KD). Surgical repair was performed with a right axillary thoracotomy approach. Proximal ligation of the sinoatrial nodal aneurysm (SNA) was performed, guided by an occlusion test. Postoperatively, P waves were absent on ECG on day 1 but reappeared by day 2. The postoperative course was uneventful.

Discussion
This case presents the youngest reported patient with the rare triad of a RCA aneurysm, SNA aneurysm, and dual coronary artery fistulas (CAF) draining into the RA. Previous reports are limited and exclusively involve adults. CAF is rare, with a prevalence of 0.002% in the population. Multiple fistulas are 10.7% to 16% of these cases. This case does not align with KD, the most common cause of coronary artery aneurysms (CAA) in children. Given the localization of lesions to the RCA and SNA instead of diffused coronary dilation, a congenital abnormality is the most plausible etiology.

Chronic shunting, even through a small CAF, can cause progressive dilation and aneurysm of the upstream level. In this infant, two giant aneurysms resulting from dual fistulas warranted surgical correction, even in the absence of heart failure or chamber dilation. This highlights the importance of considering aneurysm formation as a potential factor when evaluating the necessity for early intervention in infants.
This is also the first report of a right axillary thoracotomy for repairing complex coronary anomaly in infants. This approach, adopted at our center for congenital heart disease, offers excellent access to right-sided cardiac structures with benefits in recovery and cosmetic outcomes. Unlike reports of immediate P wave loss during temporary SNA occlusion, our patient retained P waves intraoperatively, suggesting age- or anatomy-related variation in sinus node perfusion.
  • Vo, Tue Minh  ( Hue Central Hospital , Hue , Viet Nam )
  • Nguyen, Dung Duc  ( Hue Central Hospital , Hue , Viet Nam )
  • Nguyen, Hung Xuan  ( Hue Central Hospital , Hue , Viet Nam )
  • Nguyen, Phuoc Dang  ( Hue Central Hospital , Hue , Viet Nam )
  • Dinh, Duy Tran Duy  ( Hue Central Hospital , Hue , Viet Nam )
  • Duc An Bui, Vinh  ( Hue Central Hospital , Hue , Viet Nam )
  • Dang, Chau  ( San Joaquin General Hospital , French Camp , California , United States )
  • Tran, Tam  ( Washington University School of Medicine , Saint Louis , Missouri , United States )
  • Author Disclosures:
    Tue Minh Vo: DO NOT have relevant financial relationships | Dung Duc Nguyen: No Answer | Hung Xuan Nguyen: No Answer | Phuoc Dang Nguyen: No Answer | Duy Tran Duy Dinh: No Answer | Vinh Bui: DO NOT have relevant financial relationships | Chau Dang: DO NOT have relevant financial relationships | Tam Tran: DO NOT have relevant financial relationships
Meeting Info:

Scientific Sessions 2025

2025

New Orleans, Louisiana

Session Info:

Clinical Case: Congenital and Inherited Heart Disease

Sunday, 11/09/2025 , 09:15AM - 10:10AM

Moderated Digital Poster Session

More abstracts on this topic:
Aneurysm neck width reduces flow diversion in new generation stent placed at high curvature ICA segment

Chien Aichi, Szeder Viktor, Boyle Noel, Colby Geoffrey, Duckwiler Gary

Adult-onset Kawasaki Disease: An Updated Review of the English-Language Literature from 1980 Through 2023

Adusei Poku Frank, Biney Bernice, Mensah Samuel, Ampadu Joshua Oppong, Aghasili Chukwuemeka, Oppong-twum Sandra, Baygani Shawyon, Okafor Henry

More abstracts from these authors:
Concurrent Right Coronary and Sinus Node Artery Aneurysms with Right Atrial Fistula in a Young Adult: A Case Report

Vo Tue Minh, Nguyen Dung Duc, Nguyen Hung Xuan, Nguyen Phuoc Dang, Tran Nhan Thanh Thai, Duc An Bui Vinh, Dang Chau, Tran Tam

Coccidioidal Pericarditis: Clinical Presentation, Complications, and Outcomes in Disseminated Coccidioidomycosis

Chung Duy, Le Minh, Tran Tam, Yee Erika, Dubyk Favia, Truong Vien, Le Trang Diep Thanh, Obaidi Adam, Smith Geoffrey

You have to be authorized to contact abstract author. Please, Login
Not Available